A case of paraparesis due to extramedullary haemopoiesis in HbE-thalassaemia.
نویسندگان
چکیده
A 24-year-old female with haemoglobin E-thalassaemia who presented with paraparesis of 18 months' duration was found to have spinal extradural extramedullary haemopoietic tissue extending from T4 to T9. Complete neurological recovery followed laminectomy. The importance of prompt diagnosis and treatment, of this unusual complication of extramedullary haemopoiesis, before the spinal cord is irreversibly damaged is stressed.
منابع مشابه
Spinal cord compression in thalassaemia.
Two cases of spinal cord compression resulting from extramedullary haemopoiesis in patients with thalassaemia of intermediate clinical severity are reported. The association between mild thalassaemia with long survival and the risk of spinal cord compression from extramedullary haemopoietic deposits is emphasised.
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ورودعنوان ژورنال:
- Postgraduate medical journal
دوره 53 621 شماره
صفحات -
تاریخ انتشار 1977